Groups and causes

  • PAH inherited idiopathic (BMPR2 mutation), toxics (drugs), in association with VIH, maladie de système (portal hypertension, hemolytic anemia, sclerodermia, connective tissue disorders).
  • PH caused by left-sided heart disease.
  • PH caused by lung disease : OCPD, interstitial pulmonary disease, sleep apnea syndrome, chronic altitude exposition, hypoventilation, other pulmonary disease and mixed syndrome.
  • PH caused by chronic blood clots.
  • PH associated with other conditions that have unclear reasons why the pulmonary hypertension occurs.